PULMONARY ALVEOLAR MICROLITHIASIS - REVIEW OF TURKISH REPORTS


UCAN E. S., KEYF A., AYDILEK R., YALCIN Z., SEBIT S., KUDU M., ...More

THORAX, vol.48, no.2, pp.171-173, 1993 (SCI-Expanded) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 48 Issue: 2
  • Publication Date: 1993
  • Doi Number: 10.1136/thx.48.2.171
  • Journal Name: THORAX
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Page Numbers: pp.171-173
  • Dokuz Eylül University Affiliated: Yes

Abstract

Pulmonary alveolar microlithiasis is a rare disorder, only 173 cases having been reported worldwide. Fifty two cases from Turkey are reported, 49 of which have previously been described only in Turkish publications. The mean age of the patients was 27 (SD 12) years, 34 were male, and 10 were symptomless. In 40 of the 52 cases diagnosis was confirmed histopathologically. Nineteen cases were diagnosed in siblings. This high rate suggests that pulmonary alveolar microlithiasis is a familial disease, which, though rare, is for unknown reasons most common in Turkey.