Giant angiomyolipoma associated with marked pulmonary lesions suggesting lymphangioleiomyomatosis in a patient with tuberous sclerosis.

Tüzel E., Kirkali Z., Mungan U., Cüler C., Sade M.

International urology and nephrology, cilt.32, sa.2, ss.219-22, 2000 (Scopus) identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 32 Sayı: 2
  • Basım Tarihi: 2000
  • Doi Numarası: 10.1023/a:1007183001681
  • Dergi Adı: International urology and nephrology
  • Derginin Tarandığı İndeksler: Scopus
  • Sayfa Sayıları: ss.219-22
  • Anahtar Kelimeler: Angiomyolipoma, Lymphangioleiomyomatosis, Renal neoplasms, Tuberous sclerosis
  • Dokuz Eylül Üniversitesi Adresli: Evet

Özet

The association between Tuberous Sclerosis (TS) and Angiomyolipoma (AML) is well known. A patient with TS and giant AML mimicking Renal Cell Carcinoma (RCC), measuring 29 × 18 × 11 cm, weighing 4700 gr is presented. Imaging studies revealed coexistent pulmonary lymphangioleiomyomatosis and concurrent renal and pulmonary involvement is extremely rare in patients in TS. We believe that the growth potential of this hamartomatous lesion may reach to a life threatening size.