Giant angiomyolipoma associated with marked pulmonary lesions suggesting lymphangioleiomyomatosis in a patient with tuberous sclerosis.

Tüzel E., Kirkali Z., Mungan U., Cüler C., Sade M.

International urology and nephrology, vol.32, no.2, pp.219-22, 2000 (Scopus) identifier identifier

  • Publication Type: Article / Article
  • Volume: 32 Issue: 2
  • Publication Date: 2000
  • Doi Number: 10.1023/a:1007183001681
  • Journal Name: International urology and nephrology
  • Journal Indexes: Scopus
  • Page Numbers: pp.219-22
  • Keywords: Angiomyolipoma, Lymphangioleiomyomatosis, Renal neoplasms, Tuberous sclerosis
  • Dokuz Eylül University Affiliated: Yes


The association between Tuberous Sclerosis (TS) and Angiomyolipoma (AML) is well known. A patient with TS and giant AML mimicking Renal Cell Carcinoma (RCC), measuring 29 × 18 × 11 cm, weighing 4700 gr is presented. Imaging studies revealed coexistent pulmonary lymphangioleiomyomatosis and concurrent renal and pulmonary involvement is extremely rare in patients in TS. We believe that the growth potential of this hamartomatous lesion may reach to a life threatening size.