Surgical treatment of cor triatriatum, ventricular septal defect in an infant with a giant omphalocele.

KIR M., Ugurlu B., Saylam G. S., Karadas U.

Journal of pediatric surgery, vol.46, no.7, 2011 (SCI-Expanded) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 46 Issue: 7
  • Publication Date: 2011
  • Doi Number: 10.1016/j.jpedsurg.2011.03.013
  • Journal Name: Journal of pediatric surgery
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Keywords: Cor triatriatum, Omphalocele, Ventricular septal defect, RARE
  • Dokuz Eylül University Affiliated: Yes


Cor triatriatum is a rare cardiac anomaly characterized by a membrane in the left atrium that separates the atrium into the proximal and distal chambers. Herein, we describe an unusual case of cor triatriatum combined with a ventricular septal defect in a newborn infant with a giant omphalocele and underwent a successful cardiac surgical repair. In this abnormality, there is a high incidence of associated congenital abnormalities; but to the best of our knowledge, this is the first time that a combination of cor triatriatum and omphalocele has been reported in the literature. (C) 2011 Elsevier Inc. All rights reserved.