A case of split notochord syndrome: Presence of dorsal enteric diverticulum adjacent to the dorsal enteric fistula

Akgur F., Ozdemir T., OLGUNER M., Erbayraktar S., Ozer E., Aktug T.

JOURNAL OF PEDIATRIC SURGERY, vol.33, no.8, pp.1317-1319, 1998 (SCI-Expanded) identifier identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 33 Issue: 8
  • Publication Date: 1998
  • Doi Number: 10.1016/s0022-3468(98)90179-8
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Page Numbers: pp.1317-1319
  • Keywords: split notochord syndrome, enteric diverticulum, enteric fistula, umbilical sinus
  • Dokuz Eylül University Affiliated: Yes


Like umblical enteric remnants (eg, umblical sinus and omphalomesenteric fistula), enteric remnants can be seen on the dorsal aspect of the body (dorsal enteric sinus, dorsal enteric fistula [DEF], dorsal enteric diverticulum) in conjunction with complete cleft of the vertebral column. Complete cleft of the vertebral column associated with gastrointestinal tract and central nervous system anomalies is known as "split notochord syndrome" (SNS). The authors present an unreported va riant of SNS having do rsa I enteric diverticulum adjacent to the DEF. The patient died 17 days after surgical repair. Copyright (C) 1998 by W.B. Saunders Company.