Akademik Veri Yönetim Sistemi
Turk Pediatri Arsivi, cilt.43, sa.SUPPL., ss.28-34, 2008 (Scopus, TRDizin)
This section includes the rare but well defined vasculitides of childhood. The main difference of the related disorders in our country is the frequency. Multicentered studies are needed to understand and clarify this difference. Takayasu arteritis is mostly found in young women of Asian ancestry; however, it is reported even in the first decade in childhood. Thoracic and abdominal aorta are the most involved parts in juvenile forms. Wegener granulomatosis is a necrotizing vasculitis characterized by the involvement of the small and medium sized arteries. Churg Strauss disease presents with long lasting asthma symptoms, peripheral eosinophilia and elevation of IgE. Microscopic poliangiitis is characterized by necrotizing granulomatous vasculitis of the small vessels. Hypocomplementemic urticarial vasculitis is anotner rare vasculitis in childhood. Skin biopsy is characterized by leukocytoclastic vasculitis. Cogan syndrome is another rare vasculitis of adolescence frequently involving the conjunctiva, cornea and cochlea. The main morbidity here is the hearing loss.