Retroperitoneal paragangliomas are rare neuroendocrine tumors of neural crest origin. They are mostly benign, however; malignant tumors may present aggressive behavior and may lead to metastasis. Complete surgical resection of the mass is the only potential curative treatment modality for retroperitoneal paragangliomas. Postsurgical follow-up is important for malignant potential. Here we report a case of a 18 year-old female with an 8.5 cm mass located anterior of the right kidney, treated by complete surgical excision.