A multicenter experience of thrombotic microangiopathies in Turkey: The Turkish Hematology Research and Education Group (ThREG)-TMA01 study


Tekgunduz E., YILMAZ M., ERKURT M. A., KİKİ İ., Kaya A. H., KAYNAR L., ...Daha Fazla

TRANSFUSION AND APHERESIS SCIENCE, cilt.57, sa.1, ss.27-30, 2018 (SCI-Expanded) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 57 Sayı: 1
  • Basım Tarihi: 2018
  • Doi Numarası: 10.1016/j.transci.2018.02.012
  • Dergi Adı: TRANSFUSION AND APHERESIS SCIENCE
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.27-30
  • Anahtar Kelimeler: Thrombotic microangiopathy, Thrombotic thrombocytopenic purpura, Hemolytic-uremic syndrome, TTP, HUS, HEMOLYTIC-UREMIC SYNDROME, THROMBOCYTOPENIC PURPURA, ADULT PATIENTS, DIAGNOSIS, MANAGEMENT, REGISTRY, AHUS, TTP, ECULIZUMAB, CONSENSUS
  • Dokuz Eylül Üniversitesi Adresli: Evet

Özet

Thrombotic microangiopathies (TMAs) are rare, but life-threatening disorders characterized by microangiopathic hemolytic anemia and thrombocytopenia (MAHAT) associated with multiorgan dysfunction as a result of microvascular thrombosis and tissue ischemia. The differentiation of the etiology is of utmost importance as the pathophysiological basis will dictate the choice of appropriate treatment.