Propofol infusion syndrome or adrenoleukodystrophy?

Karaman Y., Goktay A., Agin H., Karaarslan U.

PEDIATRIC ANESTHESIA, cilt.23, sa.4, ss.368-370, 2013 (SCI-Expanded) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 23 Sayı: 4
  • Basım Tarihi: 2013
  • Doi Numarası: 10.1111/pan.12113
  • Dergi Adı: PEDIATRIC ANESTHESIA
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.368-370
  • Anahtar Kelimeler: propofol, propofol infusion syndrome, adrenoleukodystrophy, ANESTHESIA
  • Dokuz Eylül Üniversitesi Adresli: Hayır

Özet

Following a propofol anesthetic, a 5-year-old girl with lower extremity spasticity seized and developed hypertriglyceridemia, hyperkalemia, and metabolic acidosis. A presumed diagnosis of propofol infusion syndrome (PRIS) was made, but further investigation revealed neonatal adrenoleukodystrophy. PRIS should be considered with this constellation of symptoms, but other neurometabolic disorders must always be ruled out.