Dermato-neuro syndrome in a case of scleromyxedema
EUROPEAN JOURNAL OF RHEUMATOLOGY, vol.2, no.4, pp.160-162, 2015 (ESCI, TRDizin)
- Publication Type: Article / Article
- Volume: 2 Issue: 4
- Publication Date: 2015
- Doi Number: 10.5152/eurjrheum.2015.0116
- Journal Name: EUROPEAN JOURNAL OF RHEUMATOLOGY
- Journal Indexes: Emerging Sources Citation Index (ESCI), TR DİZİN (ULAKBİM)
- Page Numbers: pp.160-162
- Keywords: Scleromyxedema, dermato-neuro syndrome, connective tissue
- Dokuz Eylül University Affiliated: Yes
Abstract
Scleromyxedema is an uncommon connective tissue disease characterized by mucin deposits, fibrosis, and proliferation of fibroblasts in the dermis. Although it shares similar sclerodermoid features, it is a different clinical entity than scleroderma. A monoclonal gammopathy is almost always present; however, progression to multiple myeloma is rare. It may have many systemic manifestations, of which the most notable being the dermato-neuro syndrome because of its rarity and potential fatal outcome. We present a case of a 50-year-old woman with scleromyxedema in whom the dermato-neuro syndrome developed.