Congenital upper eyelid entropion is a rare condition that does not spontaneously improve.(1) In congenital entropion, the tarsal plate loses its upright position and becomes inverted partially or entirely along the length of the lid. This condition may result in keratitis, corneal abrasion, or even ulceration and opacification. Corneal trauma makes this condition an important potential cause of corneal ulceration in infants. Since delayed recognition and treatment may result in permanent visual impairment, early diagnosis and surgical intervention are imperative.