Unusual association of neurofibromatosis Type 1 and idiopathic syringomyelia-bulbia-pontia

Cakmur R., Fadiloglu S., Pirnar T.

EUROPEAN JOURNAL OF NEUROLOGY, vol.4, no.3, pp.303-306, 1997 (SCI-Expanded) identifier identifier

  • Publication Type: Article / Article
  • Volume: 4 Issue: 3
  • Publication Date: 1997
  • Doi Number: 10.1111/j.1468-1331.1997.tb00351.x
  • Journal Name: EUROPEAN JOURNAL OF NEUROLOGY
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Page Numbers: pp.303-306
  • Keywords: neurofibromatosis type 1, syringomyelia, syringobulbia
  • Dokuz Eylül University Affiliated: Yes

Abstract

Since the association of syringomyelia and neurofibromatosis is mostly related to intramedullary tumors, syringomyelia in neurofibromatosis type 1 (NF-1) is much rarer than in neurofibromatosis type 2 (NF-2). In this paper, we present a case of NF-1 associated with an idiopathic syringomyelia extending from conus medullaris to the upper pens and discuss the relationship between neurofibromatosis and syringomyelia.