Weaning practices in phenylketonuria vary between health professionals in Europe


Pinto A., Adams S., Ahring K., Allen H., Almeida M. F., Garcia-Arenas D., ...More

MOLECULAR GENETICS AND METABOLISM REPORTS, vol.18, pp.39-44, 2019 (SCI-Expanded) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 18
  • Publication Date: 2019
  • Doi Number: 10.1016/j.ymgmr.2018.11.003
  • Journal Name: MOLECULAR GENETICS AND METABOLISM REPORTS
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Page Numbers: pp.39-44
  • Keywords: Weaning, Infant, Phenylketonuria, Phenylalanine, Phe-free infant formula, BLOOD PHENYLALANINE CONTROL, INVESTIGATING TIME BURDEN, FEEDING PRACTICES, VEGETABLES, INFANTS, FRUITS, COSTS, DIET
  • Dokuz Eylül University Affiliated: Yes

Abstract

Background: In phenylketonuria (PKU), weaning is considered more challenging when compared to feeding healthy infants. The primary aim of weaning is to gradually replace natural protein from breast milk or standard infant formula with solids containing equivalent phenylalanine (Phe). In addition, a Phe-free second stage L-amino acid supplement is usually recommended from around 6 months to replace Phe-free infant formula. Our aim was to assess different weaning approaches used by health professionals across Europe.